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European Journal of Echocardiography 2007 8(4):302-306; doi:10.1016/j.euje.2006.04.007
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Copyright © 2006, The European Society of Cardiology

Monozygotic twins with Marfan's syndrome and ascending aortic aneurysm

Héctor Jorge Redruello*, Tomas Francisco Cianciullia, Eduardo Fernandez Rostello, Barbara Recalde, Jorge Alberto Lax, Victorio Próspero Picone, Sandro Mario Belforte and Horacio Alberto Prezioso

Division of Cardiology and Cardiovascular Surgery, Hospitales del Gobierno de la Ciudad de Buenos Aires "Bernardino Rivadavia" and "Cosme Argerich", Av. Alte. Brown 240 (C1155ADP), Buenos Aires, Argentina

Received 10 January 2006; received in revised form 16 April 2006; accepted after revision 23 April 2006.

jredruello{at}hotmail.com.ar

* Corresponding author. Department of Cardiology, Hospital del Gobierno de la Ciudad de Buenos Aires "Dr. Cosme Argerich", Av. Alte. Brown 240 (C1155ADP), Buenos Aires, Argentina.


  Abstract

Marfan's syndrome is a hereditary connective tissue disease, in which cardiovascular abnormalities (especially aortic root dilatation) are the most important cause of morbidity and mortality. In this report, we describe two 24-year-old twins, with a history of surgery for lens subluxation and severe cardiovascular manifestations secondary to Marfan's syndrome. One of the twins suffered a type A aortic dissection, which required replacement of the ascending aorta, and the other twin had an aneurysmal dilatation of the ascending aorta (46mm) and was prescribed medical treatment with atenolol and periodic controls to detect the presence of a critical diameter (50mm) that would indicate the need for prophylactic surgery.

Keywords: Monozygotic twins; Marfan's syndrome; Aortic dissection; Echocardiography; Aortic root replacement

a Researcher of the Secretary of Health, Government of the City of Buenos Aires.


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