Giant Eustachian valve and left ventricular systolic dysfunction in a patient with non-dilated amyloid cardiomyopathy
Department of Cardiovascular Disease, Western Pennsylvania Hospital/Temple University Program, 4800 Friendship Avenue, Pittsburgh, PA 15224, USA
Received 7 April 2007; accepted after revision 28 April 2007; online publish-ahead-of-print 30 June 2007.
* Corresponding author. Department of Cardiovascular Disease, Suite 3411 North, Western Pennsylvania Hospital/Temple University Program, 4800 Friendship Avenue, Pittsburgh, PA 15224, USA. Tel: +1 412 578 6934, +1 412 486 3819 (Res); fax: +1 412 578 6804.E-mail address: sandeeparora24{at}hotmail.com
| Abstract |
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Amyloid cardiomyopathy is characterized by non-dilated thick-walled left ventricular, thickening of interventricular septum and right ventricular free wall, biatrial enlargement associated with granular sparkling appearance of the myocardium. Typically, decreased left ventricular compliance results in abnormal diastolic functions but left ventricular systolic functions are preserved until late in the course of the illness when left ventricle starts to dilate culminating into dilated cardiomyopathy. We present a 77-year-old patient who had typical echocardiographic features of amyloid heart disease, a giant Eustachian valve resembling cor triatriatum dexter and left ventricular systolic dysfunction without associated left ventricular dilatation.
Keywords: Restrictive cardiomyopathy; Eustachian valve; Systolic function